多囊性发育不良肾，须与隐性遗传性多囊肾区分，尽管它比隐性遗传性多囊肾常见，但本病仅散在发病，不具有明确的遗传性。囊肿较大具大小不等，通常为单侧。如果是双侧，常是不对称的，可能也会象隐性遗传性多囊肾那样，发生羊水过少及其它并发症。
This is a multicystic dysplastic kidney. This condition must be distinguished from RPKD because it occurs only sporadically and not with a defined inheritance pattern, though it is more common than RPKD. The cysts are larger and variably sized. Often, it is unilateral. If bilateral, it is often asymmetric. If bilateral, oligohydramnios and its complications can ensue, just as with RPKD.
